Hyperlipidemia
Hyperlipidemia (hyperlipemia) involves abnormally elevated levels of any or all lipids and/or lipoproteins in the blood. Hyperlipidemias may basically be classified as either familial (also called primary) caused by specific genetic abnormalities, or acquired (also called secondary) when resulting from another underlying disorder that leads to alterations in plasma lipid and lipoprotein metabolism. Also, hyperlipidemia may be idiopathic, that is, without known cause.
Hyperlipidemias are also classified according to which types of lipids are elevated, that is hypercholesterolemia, hypertriglyceridemia or both in combined hyperlipidemia. Elevated levels of Lipoprotein may also be classified as a form of hyperlipidemia.
Familial hyperlipidemias are classified according to the Fredrickson classification which is based on the pattern of lipoproteins on electrophoresis. It was later adopted by the World Health Organization (WHO). The ICD-10-CM codes are as follows:
E78.0 Pure Hypercholesterolemia (Group A) Includes: Fredickson’s hyperlipoproteinemia, type IIa; hyperbetalipoproteinemia;
low-density-lipoprotein-type [LDL] hyperlipoproteinemia
E78.1 Pure Hyperglyceridemia (Group B) Includes: pure hyperglyceridemia; elevated fasting triglycerides; endogenous
hyperglyceridemia; Fredickson’s hyperlipoproteinemia, type IV; hyperprebetalipoproteinemia; very-low-density-lipoprotein-type
[VLDL] hyperlipoproteinemia
E78.2 Mixed Hyperlipidemia (Group C) Includes: broad- or floating-betalipoproteinemia; combined hyperlipidemia NOS; elevated
cholesterol with elevated triglycerides NEC; Fredrickson’s hyperlipoproteinemia, type IIb or III; hyperbetalipoproteinemia with
prebetalipoproteinemia; hypercholesteremia with endogenous hyperglyceridemia; tubo-eruptive xanthoma; xanthoma tuberosum
E78.3 Hyperchylomicronemia (Group D) Includes: hyperchylomicronemia; mixed hyperglyceridemia; chylomicron retention
disease; Fredickson’s hyperlipoproteinemia, type I and V
E78.4 Other Hyperlipidemia Includes: Familial combined hyperlipidemia
E78.5 Hyperlipidemia, unspecified
ICD 10 and ICD 9 code for hyperlipidemia
E78.5 - Hyperlipidemia, unspecified
E78.2 - Mixed hyperlipidemia
E78.4 - Other hyperlipidemia
E78.3 - Hyperchylomicronemia
E78.0 - Pure hypercholesterolemia
E78.1 - Pure hyperglyceridemia
Hyperlipidemia (hyperlipemia) involves abnormally elevated levels of any or all lipids and/or lipoproteins in the blood. Hyperlipidemias may basically be classified as either familial (also called primary) caused by specific genetic abnormalities, or acquired (also called secondary) when resulting from another underlying disorder that leads to alterations in plasma lipid and lipoprotein metabolism. Also, hyperlipidemia may be idiopathic, that is, without known cause.
Hyperlipidemias are also classified according to which types of lipids are elevated, that is hypercholesterolemia, hypertriglyceridemia or both in combined hyperlipidemia. Elevated levels of Lipoprotein may also be classified as a form of hyperlipidemia.
Familial hyperlipidemias are classified according to the Fredrickson classification which is based on the pattern of lipoproteins on electrophoresis. It was later adopted by the World Health Organization (WHO). The ICD-10-CM codes are as follows:
E78.0 Pure Hypercholesterolemia (Group A) Includes: Fredickson’s hyperlipoproteinemia, type IIa; hyperbetalipoproteinemia;
low-density-lipoprotein-type [LDL] hyperlipoproteinemia
E78.1 Pure Hyperglyceridemia (Group B) Includes: pure hyperglyceridemia; elevated fasting triglycerides; endogenous
hyperglyceridemia; Fredickson’s hyperlipoproteinemia, type IV; hyperprebetalipoproteinemia; very-low-density-lipoprotein-type
[VLDL] hyperlipoproteinemia
E78.2 Mixed Hyperlipidemia (Group C) Includes: broad- or floating-betalipoproteinemia; combined hyperlipidemia NOS; elevated
cholesterol with elevated triglycerides NEC; Fredrickson’s hyperlipoproteinemia, type IIb or III; hyperbetalipoproteinemia with
prebetalipoproteinemia; hypercholesteremia with endogenous hyperglyceridemia; tubo-eruptive xanthoma; xanthoma tuberosum
E78.3 Hyperchylomicronemia (Group D) Includes: hyperchylomicronemia; mixed hyperglyceridemia; chylomicron retention
disease; Fredickson’s hyperlipoproteinemia, type I and V
E78.4 Other Hyperlipidemia Includes: Familial combined hyperlipidemia
E78.5 Hyperlipidemia, unspecified
ICD 10 and ICD 9 code for hyperlipidemia
E78.5 - Hyperlipidemia, unspecified
E78.2 - Mixed hyperlipidemia
E78.4 - Other hyperlipidemia
E78.3 - Hyperchylomicronemia
E78.0 - Pure hypercholesterolemia
E78.1 - Pure hyperglyceridemia
ICD-9: 272.4
E78
Excludes1: sphingolipidosis (E75.0-E75.3)
E70-E88
Excludes1: androgen insensitivity syndrome (E34.5-)
congenital adrenal hyperplasia (E25.0)
Ehlers-Danlos syndrome (Q79.6)
hemolytic anemias attributable to enzyme disorders (D55.-)
Marfan's syndrome (Q87.4)
5-alpha-reductase deficiency (E29.1)
E00-E89
ICD-9-CM Diagnosis Codes - ICD-10-CM Diagnosis Codes
272.4 Other and unspecified hyperlipidemia - E78.5 Hyperlipidemia, unspecified